Immunosuppressant agents (eg, azathioprine, cyclophosphamide)
Systemic corticosteroids (eg, prednisone)
Prescribe oxygen therapy in patients with hypoxemia at rest or with exercise (partial pressure of oxygen [PaO2] < 55 mmHg or an oxygen saturation by pulse oximetry [SpO2] < 88%). The goal is to maintain an oxygen saturation of at least 90% at rest, with sleep, and with exertion.
Encourage tobacco users to quit and offer pharmacotherapy as needed.
Vaccinate patients against influenza and pneumococcal infection.
Antifibrotic agents (eg, pirfenidone)
Tyrosine kinase inhibitors (eg, nintedanib)
